BACK
TO
TOP
Browse A-Z
Print-Friendly
Bookmarks
bookmarks-menu

Pulmonic valve stenosis

Valvular pulmonary stenosis; Heart valve pulmonary stenosis; Pulmonary stenosis; Stenosis - pulmonary valve; Balloon valvuloplasty - pulmonary

Pulmonic stenosis is a heart valve disorder that involves the pulmonary valve.

This is the valve separating the right ventricle (one of the chambers in the heart) and the pulmonary artery. The pulmonary artery carries oxygen-poor blood to the lungs.

Stenosis, or narrowing, occurs when the valve cannot open wide enough. As a result, blood flows less easily to the lungs.

Causes

Narrowing of the pulmonary valve is most often present at birth (congenital). It is caused by a problem that occurs as the baby develops in the womb before birth. The cause is unknown, but genes may play a role.

Narrowing that occurs in the valve itself is called valvular pulmonic stenosis. There may also be narrowing just before or after the valve.

The defect may occur alone or with other heart defects that are present at birth. The condition can be mild or severe.

Pulmonic stenosis is a rare disorder. In some cases, the problem runs in families.

Symptoms

Many cases of pulmonic stenosis are mild and do not cause symptoms. The problem is most often found in infants when a heart murmur is heard during a routine heart exam.

When the valve narrowing (stenosis) is moderate to severe, the symptoms include:

Symptoms may get worse with exercise or activity.

Exams and Tests

The health care provider may hear a heart murmur when listening to the heart using a stethoscope. Murmurs are blowing, whooshing, or rasping sounds heard during a heartbeat.

Tests used to diagnose pulmonary stenosis may include:

The provider will grade the severity of the valve stenosis to plan treatment.

Treatment

Sometimes, treatment may not be needed if the disorder is mild.

When there are also other heart defects, medicines may be used to:

  • Help blood flow through the heart (prostaglandins)
  • Help the heart beat stronger
  • Prevent clots (blood thinners)
  • Remove excess fluid (water pills)
  • Treat abnormal heartbeats and rhythms

Percutaneous balloon pulmonary dilation (valvuloplasty) may be performed when no other heart defects are present.

  • This procedure is done through an artery in the groin.
  • The doctor sends a flexible tube (catheter) with a balloon attached to the end up to the heart. Special x-rays are used to help guide the catheter.
  • The balloon stretches the opening of the valve.

Some people may need heart surgery to repair or replace the pulmonary valve. The new valve can be made from different materials. If the valve cannot be repaired or replaced, other procedures may be needed.

Outlook (Prognosis)

People with mild disease rarely get worse. However, those with moderate to severe disease will get worse. The outcome is often very good when surgery or balloon dilation is successful. Other congenital heart defects may be a factor in the outlook.

Most often, the new valves can last for decades. However, some will wear out and need to be replaced.

Possible Complications

Complications may include:

  • Abnormal heartbeats (arrhythmias)
  • Death
  • Heart failure and enlargement of the right side of the heart
  • Leaking of blood back into the right ventricle (pulmonary valve regurgitation) after repair

When to Contact a Medical Professional

Contact your provider if:

  • You have symptoms of pulmonary valve stenosis.
  • You have been treated or have untreated pulmonary valve stenosis and have developed swelling (of the ankles, legs, or abdomen), difficulty breathing, or other new symptoms.
Open References

References

Carabello BA, Kodali S. Valvular heart disease. In: Goldman L, Cooney KA, eds. Goldman-Cecil Medicine. 27th ed. Philadelphia, PA: Elsevier; 2024:chap 60.

Pellikka PA, Nkomo VT. Tricuspid, pulmonic, and multivalvular disease In: Libby, P, Bonow RO, Mann DL, Tomaselli, GF, Bhatt DL, Solomon SD, eds. Braunwald's Heart Disease: A Textbook of Cardiovascular Medicine. 12th ed. Philadelphia, PA: Elsevier; 2022:chap 77.

Sharkey A, Choudhury N, Mahmood F. Valvular heart disease. In: Hines RL, Jones SB, eds. Stoelting's Anesthesia and Co-Existing Disease. 8th ed. Philadelphia, PA: Elsevier; 2022:chap 6.

Therrien J, Marelli AJ. Congenital heart disease in adults. In: Goldman L, Cooney KA, eds. Goldman-Cecil Medicine. 27th ed. Philadelphia, PA: Elsevier; 2024:chap 61.

Valente AM, Dorfman AL, Babu-Narayan SV, Krieger EV. Congenital heart disease in the adolescent and adult. In: Libby, P, Bonow RO, Mann DL, Tomaselli, GF, Bhatt DL, Solomon SD, eds. Braunwald's Heart Disease: A Textbook of Cardiovascular Medicine. 12th ed. Philadelphia, PA: Elsevier; 2022:chap 82.

  • Valvular heart disease (VHD) overview

    Valvular heart disease (VHD) overview

    Animation

    •  

    Valvular heart disease (VHD) overview - Animation

    Valvular heart disease (VHD) describes any abnormality of the heart valves, including the valves on the left side of the heart: mitral and aortic valves, and the valves on the right side of the heart: the tricuspid and pulmonary valves. In a normally functioning heart, valves ensure that blood flows in only one direction and at the right time. The valves act like gates that swing open to allow blood flow and then shut tightly until the next cycle begins. Valvular heart disease consists of two types of abnormalities: stenosis, where the valve does not open completely impairing forward blood flow, and regurgitation, where the valve does not close completely allowing reversed blood flow. Abnormal blood flow often produces atypical heart sounds known as murmurs. The most common causes of valvular disease include infective endocarditis, rheumatic fever, congenital malformations, and trauma. Predisposing factors include hypertension, myocardial infarction, coronary artery disease, pregnancy, anemia, and infection. Treatment of valvular diseases often includes a combination of lifestyle changes, drug therapy, balloon valvuloplasty, or valve replacement surgery depending on the severity.

  • Heart valves

    Heart valves - illustration

    The valves of the heart open and close to control the flow of blood entering or leaving the heart.

    Heart valves

    illustration

  • Valvular heart disease (VHD) overview

    Animation

    •  

    Valvular heart disease (VHD) overview - Animation

    Valvular heart disease (VHD) describes any abnormality of the heart valves, including the valves on the left side of the heart: mitral and aortic valves, and the valves on the right side of the heart: the tricuspid and pulmonary valves. In a normally functioning heart, valves ensure that blood flows in only one direction and at the right time. The valves act like gates that swing open to allow blood flow and then shut tightly until the next cycle begins. Valvular heart disease consists of two types of abnormalities: stenosis, where the valve does not open completely impairing forward blood flow, and regurgitation, where the valve does not close completely allowing reversed blood flow. Abnormal blood flow often produces atypical heart sounds known as murmurs. The most common causes of valvular disease include infective endocarditis, rheumatic fever, congenital malformations, and trauma. Predisposing factors include hypertension, myocardial infarction, coronary artery disease, pregnancy, anemia, and infection. Treatment of valvular diseases often includes a combination of lifestyle changes, drug therapy, balloon valvuloplasty, or valve replacement surgery depending on the severity.

  • Heart valves

    Heart valves - illustration

    The valves of the heart open and close to control the flow of blood entering or leaving the heart.

    Heart valves

    illustration

 

Review Date: 5/13/2024

Reviewed By: Mary C. Mancini, MD, PhD, Cardiothoracic Surgeon, Shreveport, LA. Review provided by VeriMed Healthcare Network. Also reviewed by David C. Dugdale, MD, Medical Director, Brenda Conaway, Editorial Director, and the A.D.A.M. Editorial team.

The information provided herein should not be used during any medical emergency or for the diagnosis or treatment of any medical condition. A licensed medical professional should be consulted for diagnosis and treatment of any and all medical conditions. Links to other sites are provided for information only -- they do not constitute endorsements of those other sites. No warranty of any kind, either expressed or implied, is made as to the accuracy, reliability, timeliness, or correctness of any translations made by a third-party service of the information provided herein into any other language. © 1997- A.D.A.M., a business unit of Ebix, Inc. Any duplication or distribution of the information contained herein is strictly prohibited.
© 1997- adam.comAll rights reserved.

 
 
 

 

 

A.D.A.M. content is best viewed in IE9 or above, Firefox and Google Chrome browser.
Content is best viewed in IE9 or above, Firefox and Google Chrome browser.